Cic edizioni internazionali
Clinical Dermatology

A case of oral dermatofibrosarcoma protuberans relapsing in the skin

Case-based review, 26 - 28
Tag this article
Abstract
Enhanced HTML Full text PDF
Dermatofibrosarcoma protuberans comprises roughly 0.1% of all malignant tumors and approximately 1 to 2 percent of all soft tissue sarcomas. Slowly growing and locally aggressive, dermatofibrosarcoma protuberans can reach an enormous size, underlying in fascia and musculoskeletal structures including bone and also becoming superficial. It is characterized by high rates of local recurrence and low risk of metastasis. Dermatofibrosarcoma protuberans may involve the head and neck area in 10-15% of cases, but it is rarely described in the oral mucosa.
Here, we describe a case of oral dermatofibrosarcoma protuberans relapsing in the skin after 18 years. The lineage of the cell type comprising dermatofibrosarcoma protuberans remains a matter of controversy, but this case is consistent with the opinion that the progenitor cell is not only present in the skin but also in the submucosal tissue of the oral cavity.

Vol. 7 (No. 2) 2019 April - June

  1. A case report of atypical presentation of pyoderma gangrenosum with ulcerative colitis: successful treatment with prednisolone and mesalazine therapy
    Abou-Taleb D. A.E, F. Sherif M., Mohammed A.S.
  2. Histopathological coexistence of extragenital lichen sclerosus and morphea in a single lesion: a case report
    Almuqati R., Hariri J., Abduljabbar M.
  3. Hedgehog pathway inhibitors for basal cell carcinoma: case reports and review of the literature
    Singer C., O’Sullivan N.-A., Vinciullo C.
  4. Sirolimus therapy for refractory kaposiform hemangioendothelioma with Kasabach-Merritt phenomenon: a case report
    Valsassina R., Contreiras M., Strecht J., Melo F., Oom P.
  5. Superimposed Mongolian spot and mucopolysaccharidosis VI
    Ribeiro E.M., Ribeiro Fontenele Bezerra K., César Cardoso-dos-Santos A., Lourenço C.M., Kiszewski A.E.
  6. First reported case of primary peritoneal malignancy with initial presentation as cutaneous metastases
    Wong V., Tharakaram S., Kontogiorgi D., Shahzad J., Burova E., Maidment G., Smith S., Vohra V.
Last Viewed articles: la lista degli ultimi x visitati.
  1. A case of oral dermatofibrosarcoma protuberans relapsing in the skin
    Corradin M.T., Forcione M., Giuliani E., Fiorentino R., Zarian H., Marinello E., Alaibac M.
credits