Cic edizioni internazionali
Clinical Dermatology

A case of oral dermatofibrosarcoma protuberans relapsing in the skin

Case-based review, 26 - 28
Tag this article
Abstract
Enhanced HTML Full text PDF
Dermatofibrosarcoma protuberans comprises roughly 0.1% of all malignant tumors and approximately 1 to 2 percent of all soft tissue sarcomas. Slowly growing and locally aggressive, dermatofibrosarcoma protuberans can reach an enormous size, underlying in fascia and musculoskeletal structures including bone and also becoming superficial. It is characterized by high rates of local recurrence and low risk of metastasis. Dermatofibrosarcoma protuberans may involve the head and neck area in 10-15% of cases, but it is rarely described in the oral mucosa.
Here, we describe a case of oral dermatofibrosarcoma protuberans relapsing in the skin after 18 years. The lineage of the cell type comprising dermatofibrosarcoma protuberans remains a matter of controversy, but this case is consistent with the opinion that the progenitor cell is not only present in the skin but also in the submucosal tissue of the oral cavity.

Vol. 5 (No. 3-4) 2017 July - December

  1. Comparison of two skincare regimens in healthy newborns during the first six weeks of life
    Theunis J., Villeneuve C., Bianchi P., Bacquey A., Casas C., Mengeaud V., Kanti V., Schmitt A.M., Blume-Peytavi U., Garcia Bartels N.
    doi: 10.11138/cderm/2017.5.3.099
  2. Cutaneous inflammatory pseudotumour: a rare and multimorphic condition
    Naimer S.A., Vlodavsky E.
    doi: 10.11138/cderm/2017.5.3.107
  3. Localized sarcoidosis in an old tattoo: Illustrating the principle of locus minoris resistentiae
    Coromilas A.J., Foreman R.K., Chen S.T.
    doi: 10.11138/cderm/2017.5.3.111
  4. Secondary syphilis with granulomatous histology. A diagnostic challenge
    Drumm C., Tait C.P.
    doi: 10.11138/cderm/2017.5.3.115
  5. Psoriatic uveitis is not an exploded myth
    Gallenga C.E., Parmeggiani F., Monari P., Perri P.
    doi: 10.11138/cderm/2017.5.3.118
Last Viewed articles: la lista degli ultimi x visitati.
  1. A case of oral dermatofibrosarcoma protuberans relapsing in the skin
    Corradin M.T., Forcione M., Giuliani E., Fiorentino R., Zarian H., Marinello E., Alaibac M.
credits